Population‐Based Study of Prenatal Detection of Critical Congenital Heart Disease in Kyu‐Yama Region of Japan
Rattachement africain : jp, us. Niveau de preuve : code pays fourni par la source.
Le résumé fourni par la source
BACKGROUND: The prenatal detection rate (PDR) of congenital heart disease (CHD) has been scarcely reported in Japan. This study aimed to investigate PDR of critical CHD in a region of Japan and to evaluate the impact of prenatal diagnosis on postnatal mortality and severe morbidity. MATERIALS AND METHODS: We included patients diagnosed with CHD either prenatally and postnatally between January 1st 2018 and December 31st 2020, based on the institutional database. The Kyu-Yama region comprises the seven prefectures of Kyushu island, Yamaguchi prefecture, and Okinawa prefecture. Clinical outcome was compared with prenatal versus postnatal diagnosis. RESULTS: The overall PDR of critical CHD in the region was 64% (400 of 626 cases). Fifty-four (14%) fetuses were diagnosed within 22 weeks of gestational age. Among these cases, termination of pregnancy was selected in 5 (1%) cases. In subgroup analyses by CHD type, heterotaxy had the highest detection rate (91%), followed by hypoplastic left heart syndrome (86%). In contrast, lower detection rates were observed in transposition of the great arteries (43%) and total anomalous pulmonary venous connection (15%). Detection rates varied by prefectures, ranging from 41% to 75%. Among actively managed cases, overall, there was a significant difference in mortality and severe morbidity between prenatal and postnatal groups [66 (18%) vs. 20 (9%), p = 0.0031]. CONCLUSION: The overall PDR in this regional cohort was favorable; however, substantial differences remained across prefectures and CHD types. Reducing these disparities may require guideline-based education. Further research is warranted to clarify the prognostic impact of prenatal diagnosis.
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Le contrôle bibliographique ouvert
DOI retrouvé dans Crossref DOI retrouvé ; titre concordant.
- Titre Crossref
- Population‐Based Study of Prenatal Detection of Critical Congenital Heart Disease in Kyu‐Yama Region of Japan
- Date Crossref
- 01/01/2026
- Éditeur
- Wiley
- Type
- journal-article
Ce recoupement confirme des métadonnées liées au DOI. Il ne confirme ni la méthode ni les conclusions de l’étude, et il ne compte pas comme une seconde source scientifique indépendante.
Où se fait cette recherche
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Kyushu University Department of Pediatrics pays non établi dans la noticeUniversité ou école supérieure
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Fukuoka Children's Hospital and Medical Center for Infectious Diseases pays non établi dans la noticeÉtablissement de santé
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Oita Prefectural Hospital pays non établi dans la noticeÉtablissement de santé
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Oita University Hospital pays non établi dans la noticeÉtablissement de santé
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Kagoshima University Hospital pays non établi dans la noticeÉtablissement de santé
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Kyushu Hospital pays non établi dans la noticeÉtablissement de santé
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Japan Community Healthcare Organization pays non établi dans la noticeOrganisme public
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University of Miyazaki Division of Pediatrics pays non établi dans la noticeUniversité ou école supérieure
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University of Miyazaki Hospital pays non établi dans la noticeÉtablissement de santé
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Yamaguchi University pays non établi dans la noticeUniversité ou école supérieure
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Children's Medical Center pays non établi dans la noticeÉtablissement de santé
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Saga University pays non établi dans la noticeUniversité ou école supérieure
Department of Pediatrics — Kyushu University, Fukuoka Children's Hospital and Medical Center for Infectious Diseases et Oita Prefectural Hospital, avec 9 autres affiliations.
Une affiliation ne permet pas de déduire la nationalité d’un auteur.