Accès ouvert
2026
article
OpenAlex
Joanna Nowacka-Ejsmont, Karol Bączek, Iwona Bestry, Katarzyna Błasińska et autres
INTRODUCTION: Sirolimus is a standard disease‑modifying therapy for lymphangioleiomyomatosis (LAM), but long‑term routine‑care data integrating pulmonary, lymphatic, extrapulmonary, and biomarker outcomes remain limited. OBJECTIVES: Our aim was to assess long‑term effectiveness and safety of sirolimus in routine clinical practice. PATIENTS AND METHODS: …
ir, ge, pl, es
(code pays fourni par la source)
2024
conference-abstract
OpenAlex
Elżbieta Radzikowska, K. Blasinska, R. Langfort, P. Skronska et autres
pl, es
(code pays fourni par la source)
2020
conference-abstract
OpenAlex
Elżbieta Radzikowska, Joanna Nowacka-Ejsmont, Joanna Miłkowska-Dymanowska, Elżbieta Wiatr et autres
Lymphangioleiomyomatosis (LAM) is a rare disease caused by proliferation of abnormal smooth muscle-like cells, which can result in polycystic lungs destruction, formation of renal angiomyolipomas, lymphadenopathy, cystic lymphangiomas, abdominal lymphangioleiomyomas, chylothorax, and chyloperitoneum. The disease affects mainly women in childbearing age and …
pl, es
(code pays fourni par la source)
2010
article
OpenAlex
Jacek Dadan, Agnieszka Nowacka, Joanna Nowacka-Ejsmont
We’ve built this digital research platform to provide academics everywhere with fast, stable and secure digital access to our library of over 110,000 scholarly books and 800,000 journal articles. We’ve tested the platform in close cooperation with leading academic institutions. If you …
2010
article
OpenAlex
Jacek Dadan, Agnieszka Nowacka, Joanna Nowacka-Ejsmont
pl
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