Lung transplantation for ultra-rare diseases: from anecdote to evidence, a collective responsibility

Le résumé fourni par la source

Extract The role of lung transplantation (LTx) in patients with ultra-rare lung diseases has long been constrained by a fundamental paradox: while transplantation may be the only available life-saving treatment at the terminal phase, the scarcity of cases has historically precluded the generation of robust evidence, forcing clinicians to make decisions based on anecdotal cases and experience acquired by individual centres. In pulmonary alveolar proteinosis (PAP), diagnostic and therapeutic approaches have improved remarkably over the past two decades, resulting in significant survival gains.

Ce résumé expose les affirmations des auteurs. BNTIC ne l’interprète pas comme une validation indépendante des résultats.