A rare splenic and pancreatic inflammatory myofibroblastic tumour with left‑sided portal hypertension and gastric varices: A case report

Résumé fourni par la source

Left-sided portal hypertension or segmental portal hypertension is a rare cause of upper gastrointestinal bleeding. The present study reports a case of isolated gastric variceal haemorrhage and hypersplenism, due to left-sided portal hypertension induced by inflammatory myofibroblastic tumour (IMT)-associated splenic vein compression. IMT is an rare mesenchymal neoplasm of intermediate malignant potential that can develop in any location, frequently remaining entirely asymptomatic until it reaches a size that leads to complications. To the best of our knowledge, this is the first case reported of an IMT involving both the spleen and the pancreas. In this patient, splenectomy and partial pancreatectomy were both diagnostic and curative for IMT, and no adjuvant therapy was followed. This case report, along with a short review of the current knowledge on IMT features, contributes towards the understanding and diagnosis of this rare entity with diverse clinical presentations.

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