A Unique Case with Tracheal Atresia Among Published Literature on TACRD and VACTERL Associations

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Despite advances in surgical treatment methods, the mortality rate in TA is high, and about 85% of children with TA die within two days after birth (2) .The diagnosis is often made at post-mortem examination. Concomitanttracheo-esophageal or bronchoesophageal fistulas allow ventilation and resuscitation after esophageal intubation.After birth, a timely diagnosis and effective airway treatment are essential for patients' survival (3) .Although the cause of TA is still unknown, it is often associated with the components of TACRD (tracheal agenesis, cardiac, renal and duodenal malformations) and VACTERL (vertebral anomalies, anal atresia, cardiovascular anomalies, trachea-esophageal fistula (TEF), esophageal atresia, renal/radial anomalies, limb defects) associations (4) .In this study, a female newborn ABSTRACT Tracheal atresia/agenesis (TA) is associated with other congenital anomalies (TACRD and/or VACTERL).In this study, a female newborn with TA who had all the elements associated with TACRD and VACTERL was reported.The patient with TA, tracheo-esophageal fistula (TEF) connecting to the esophagus at the level of the carina, persistent left superior vena cava, duodenal atresia, vertebral and limb defects, bilateral hydronephrosis, and persistent cloaca was operated on postnatal 5 th day.Band ligation to the abdominal esophagus, gastrostomy, duodenal atresia repair and diverting colostomy due to persistent cloaca were performed.The lungs were bilaterally expanded in the first postnatal, preoperative and postoperative chest radiographs.Oxygen saturation remained above 90% until the patient died suddenly on the postnatal 8 th day.TA is a very rare congenital anomaly that causes postnatal respiratory distress.This case is unique among the literature on TACRD and VACTERL associations for many reasons.Esophageal band ligation in TA cases with TEF is a method that keeps the pressure in the esophagus at an appropriate level and provides air passage to the trachea via fistula. Keywords: Duodenal atresia,

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